Macrodactyly (Local gigantism)

Macrodactyly.

We report the results of the treatment of 23 patients with macrodactyly. Eighteen had a two-stage bulk-reducing (defatting) procedure; phalangectomy was used to shorten the digits. At a mean follow-up of nine years (2 to 12), two patients had been lost to follow-up, and three await a second-stage procedure. Good cosmetic correction was achieved in 12 patients, with satisfactory results in seven...

A Case of Congenital Local Gigantism

Report of a case of Proteus syndrome with severe anemia

Proteus syndrome is a rare congenital disorder comprised of subcutaneous and internal hamartomas, miscellaneous skin and vascular nevi, skeletal and nervous system and eye malformations, with characteristic manifestations including hemihypertrophy, local gigantism, macrodactyly and cerebriform thickness of soles and palms. A 23 year-old man with diagnosis of proteus syndrome had sever ane...

Congenital macrodactyly: a clinical study.

Congenital macrodactyly is a rare congenital malformation characterised by progressive enlargement of all mesenchymal elements of a digit. The present study is an attempt to draw the attention towards the similarities and differences between macrodactyly of the hand and foot. Radiographical, operative findings and histopathological examination of five cases are included in the present study. Em...

A Case of Macrodactyly

S., a Hindu girl, aged 10 years, of the village Saraiyan, in Ghazipnr district, was admitted into the hospital with abnormal enlargement of the right middle finger. She came to the hospital for its removal, as she had been feeling its weight. It is seven and a half inches in length and seven and a half inches in diameter at its thickest part. The left middle finger is three inches in length and...